Hirschsprung s disease, usually diagnosed in newborns, is a birth defect that affects about l out of 5,000 individuals. Parkinsons disease handbook american parkinson disease. Eighty nine patients, clinically and radiologically diagnosed with hirschsprungs disease underwent surgery and were included in the study. C 17 serial rectal irrigation should be performed before surgery to help prevent enterocolitis. Also, it is known as aganglionosis because one of the main characteristics in all these patients is that they do not have ganglion cells in the rectum. Hirschsprung s disease should be confirmed using rectal suction biopsy. Children who have surgery for hirschsprung disease most often feel better after surgery. It is a functional rather than mechanical obstruction caused by maldevelopment of the enteric nervous system and surgery is usually required to alleviate the obstruction. Hirschsprung disease is a lifethreatening illness, and treatment requires surgery. Hirschsprungs disease in neonates with special reference to. A child with hirschsprung disease without complications should be followed regularly to at least age 5 years, and the pa should observe for signs of longterm postoperative complications. Deepak singh and others published role of barium enema in the diagnosis of.
The utility of the hematoxylin and eosin staining in. Those affected with this birth defect are missing intestinal nerve cells called ganglion cells. In this procedure, the lining of the diseased part of the colon is stripped away. Neonatal congenital microvillus atrophy postgraduate medical. The surgical treatment of hirschsprung s disease in the adult or adolescent adult hirschsprung s disease remains controversial. Hirschsprung s hirshsproongz disease is a condition that affects the large intestine colon and causes problems with passing stool. Hirschsprungs disease symptoms and causes mayo clinic.
These nerve cells allow the intestine to relax so stool poop can pass through the intestine and out of the body. For most people, hirschsprung s disease is treated with surgery to bypass the part of the colon thats lacking nerve cells. Doctors will usually do one of two types of surgery. Currently, apart from preventiontreatment of dehydration.
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